What is fire disease?
FIRES stands for febrile infection-related epilepsy syndrome. It is sometimes also called febrile illness-related epilepsy syndrome and was previously called fever induced refractory epileptic encephalopathy in school-aged children.
What is fire epilepsy?
FIRES is a rare chronic epilepsy syndrome that suddenly develops after an acute febrile illness. A child will develop frequent and progressively debilitating seizures within a few weeks after a febrile illness such as those from a minor upper respiratory illness or a gastrointestinal bug.
What is Norse syndrome?
New-onset refractory status epilepticus (NORSE) is defined as a condition, not a specific diagnosis, with new onset of refractory status epilepticus without a clear acute or active structural, toxic or metabolic cause in a patient without active epilepsy.
Are fires curable?
Treatment of FIRES is difficult, typically unresponsive to antiepileptic drugs. Some children resolve temporarily with drug-induced burst suppression comas. Other therapies such as a ketogenic diet have limited benefit.
How do you treat Norse?
There is currently no known specific therapy for NORSE and studies are urgently needed to determine what the best treatment options are. The treatment of SE initially consists of benzodiazepines (lorazepam, diazepam, or clonazepam), followed by a standard anticonvulsant medication, as in most cases of SE.
What are the most serious complications associated with status epilepticus?
Acute complications result from hyperthermia, pulmonary edema, cardiac arrhythmias, and cardiovascular collapse. Long-term complications include epilepsy (20% to 40%), encephalopathy (6% to 15%), and focal neurologic deficits (9% to 11%).
What is Rasmussen encephalitis?
Rasmussen encephalitis, sometimes referred to as Rasmussen syndrome, is a rare disorder of the central nervous system characterized by chronic progressive inflammation (encephalitis) of one cerebral hemisphere.
Is favorable outcome possible after prolonged refractory status epilepticus?
In many series, prolonged, refractory SE has a mortality of 30% to 50%, and several studies indicate that most survivors have a substantial decline in functional status. Nevertheless, several reports demonstrate that good functional outcome is possible even after several days of SE and coma induction.
What is fire curing?
The fire-curing process resembles air curing except that open wood fires are kindled on the floor of the curing barn after the tobacco has been hanging for two to six days. The smoke imparts to the tobacco a characteristic aroma of creosote.
What does fires mean in the Army?
Fires is the related tasks and systems that provide collective and coordinated use of Army indirect fires, air and missile defense, and joint fires through the targeting process. Alternatively, it can be defined as the use of weapon systems to create a specific lethal or nonlethal effect on a target.
What is the prognosis of febrile infection-related epilepsy syndrome (FIRES)?
Poor, 82% of patients experience some level of permanent intellectual disability ranging from mild to vegetative state. Febrile infection-related epilepsy syndrome (FIRES) is an epilepsy syndrome in which new-onset refractory status epilepticus (NORSE) is preceded by febrile illness 24 hours to 2 weeks prior to the onset of seizures.
How common is fires syndrome?
The syndrome is very rare: it may only affect 1 in 1,000,000 children. FIRES starts with a febrile illness up to two weeks before seizure onset. These seizures damage the frontal lobe’s cognitive brain function such as memory and sensory abilities.
What is Firfires syndrome?
FIRES stands for febrile infection-related epilepsy syndrome. It is sometimes also called febrile illness-related epilepsy syndrome and was previously called fever induced refractory epileptic encephalopathy in school-aged children. It usually affects school-aged children with an average age of 8 years old.
What is fires and what are the symptoms?
What is FIRES? FIRES stands for febrile infection-related epilepsy syndrome. It is sometimes also called febrile illness-related epilepsy syndrome and was previously called fever induced refractory epileptic encephalopathy in school-aged children. It usually affects school-aged children with an average age of 8 years old.