What is restrictive cardiomyopathy?
Restrictive cardiomyopathy (RCM) is a condition where the chambers of the heart become stiff over time. Though the heart is able to squeeze well, it’s not able to relax between beats normally. This makes it harder for the heart to fill with blood.
What are the 3 types of cardiomyopathy?
The main types of cardiomyopathy include dilated, hypertrophic and restrictive cardiomyopathy. Treatment — which might include medications, surgically implanted devices, heart surgery or, in severe cases, a heart transplant — depends on which type of cardiomyopathy you have and how serious it is.
What are some causes of restrictive cardiomyopathy?
Other causes of restrictive cardiomyopathy include:
- Cardiac amyloidosis.
- Carcinoid heart disease.
- Diseases of the heart lining (endocardium), such as endomyocardial fibrosis and Loeffler syndrome (rare)
- Iron overload (hemochromatosis)
- Sarcoidosis.
- Scarring after radiation or chemotherapy.
- Scleroderma.
- Tumors of the heart.
How common is restrictive cardiomyopathy?
Restrictive cardiomyopathy is a rare condition. The most common causes are amyloidosis and scarring of the heart from an unknown cause. It also can occur after a heart transplant.
How is amyloidosis-induced restrictive cardiomyopathy treated?
Reduced QRS voltage on EKG may be an indicator of amyloidosis-induced restrictive cardiomyopathy. Treatment of restrictive cardiomyopathy should focus on management of causative conditions (for example, using corticosteroids if the cause is sarcoidosis), and slowing the progression of cardiomyopathy.
What is restrictive cardiomyopathy (RCM)?
Micrograph of cardiac amyloidosis, a cause of restrictive cardiomyopathy. Congo red stain. Restrictive cardiomyopathy ( RCM) is a form of cardiomyopathy in which the walls of the heart are rigid (but not thickened). Thus the heart is restricted from stretching and filling with blood properly.
What is the rate of incidence for cardiac amyloidosis?
This relatively rare form of cardiac amyloidosis occurs in an estimated six to ten cases per 1,000,000 people. This sub- type usually affects males over the age of 60 and is rapidly progressive. Pathogenesis of this form is due to the aggregation of immunoglobulin lambda light chains.
What is non-compaction cardiomyopathy?
Non-compaction cardiomyopathy (NCCMP) LV wall has a spongy appearance. Jenni criteria (Heart 2007). Also called insulated non compaction of the ventricular myocardium (INVM), it is a rare form of congenital heart disease in which the tissue of the ventricular myocardium is not well constructed in terms of texture.