What is the treatment for pulmonary atresia?
Usually, the child will need surgery to treat the heart defect and help improve blood flow to the lungs. As a temporary measure, newborns with pulmonary atresia are usually given an intravenous drug (injected into a vein) called alprostadil (Prostin VR Pediatric®) to prevent the ductus arteriosus from closing.
What is tetralogy of Fallot with pulmonary atresia and MAPCAs?
Tetralogy of Fallot with pulmonary valve atresia and major aortopulmonary collateral arteries (TOF/PA/MAPCAs) is the most extreme variant of TOF, in which complete atresia of the pulmonary valve replaces pulmonary stenosis.
What are the steps involving the repair of tetralogy of Fallot?
Surgery involves widening or replacing the pulmonary valve and enlarging the passage from the right ventricle to the pulmonary artery. This improves blood flow to the lungs. Surgeons also close the VSD with a patch. The patch stops oxygen-rich and oxygen-poor blood from mixing between the ventricles.
Can tetralogy of Fallot be corrected?
Tetralogy of Fallot can be corrected with surgery. This is generally done during the first year of life, though occasionally it can be done at an older age.
What is PA band surgery?
Pulmonary artery banding (PAB) is a palliative surgical technique used for the correction of congenital cardiac defects, characterized by pulmonary over-circulation caused by left-to-right shunting of blood. PAB is reserved for palliation in a certain subset of infants with complex congenital heart disease.
What are the complications of tetralogy of Fallot?
What are possible complications of tetralogy of Fallot?
- Blood clots (which may be in the brain causing stroke)
- Infection in the lining of the heart and heart valves (bacterial endocarditis)
- Abnormal heart rhythms (arrhythmias)
- Heart failure.
- Death.
What is ICR surgery?
For those with congenital heart disease (CHD) associated with pulmonary hypertension (PH), a 2-stage procedure of pulmonary artery banding (PAB) and then intracardiac repair (ICR) in early infancy is performed to prevent such pulmonary vascular diseases in early infancy.
How much does TOF surgery cost?
The researchers also adjusted cost savings for patient to see the figures if all centers performed as well as lowest cost quartiles. The estimated numbers were: $3,741 for ASD repair, $6,323 for VSD repair, $5,789 for TOF and $12,846 for ASO.
What is the optimal age for repair of tetralogy of Fallot?
The best survival and physiological outcomes were achieved with primary repair in children aged 3 to 11 months. Conclusions—On the basis of mortality and physiological outcomes, the optimal age for elective repair of tetralogy of Fallot is 3 to 11 months of age.
How is PA banding done?
The band is wrapped around the main pulmonary artery and fixed into place. Once inserted, the band is tightened, narrowing the diameter of the pulmonary artery to reduce blood flow to the lungs and reduce pulmonary artery pressure.